Asymptomatic girl, 6 years old. Echocardiogram: possibly sinus venosus type defect near the inferior vena cava. The CXR (see above) suggests the diagnosis of an anomalous right (lower) pulmonary vein draining into the IVC (scimitar syndrome). This is confirmed in the cathlab:
The intraoperative findings confirmed the anomalous pulmonary vein draining into the IVC at the level of the diaphragm. After creating an ASD an intracaval/intraatrial tunnel was fashioned from autologous glutaraldehyde fixated pericardium to redirect the pulmonary venous blood into the left atrium. The child recovered well. The channel is widely patent on follow up echocardiography.
last update Sept 21, 1999